Subacute sclerosing panencephalitis: A clinical appraisal

Subacute Sclerosing Panencephalitis in Iran

Subacute Sclerosing Panencephalitis in Iran. Clinical and immunoligical characlerisation

[Subacute sclerosing panencephalitis].

Subacute sclerosing panencephalitis is a slowly progressive neurodegenerative disorder occurring in childhood and adolescence and is characterised by dementia, ataxia, myoclonias and other neurological focal signs, with an invariably fatal outcome. The author reviews the subject, focussing on epidemiology, clinical features, measles virus behaviour, host immune reactions, measles prophylaxis an...

Subacute sclerosing panencephalitis.

Introduction Subacute sclerosing panencephalitis (SSPE) is a rare disease which predominantly affects children of school age. The clinical features include an insidious afebrile onset with behavioural disturbance and progressive dementia sometimes associated with epilepsy. Later akinetic mutism and myoclonic jerks with pyramidal and extrapyramidal signs appear. Finally there is progressive deco...

Subacute sclerosing panencephalitis: clinical and demographic characteristics.

OBJECTIVE To determine the clinical and demographic characteristics of children diagnosed with Subacute sclerosing panencephalitis (SSPE). STUDY DESIGN Case series. PLACE AND DURATION OF STUDY The Aga Khan University Hospital, Karachi, from January 2000 to June 2012. METHODOLOGY A retrospective analysis was done, regarding medical charts of 43 children under the age of 16 years with a dis...